|
1 / 1
|
DeCS
|
|
 |
|
Descriptor English:
|
|
Ichthyosiform Erythroderma, Congenital
|
|
Descriptor Spanish:
|
|
Eritrodermia Ictiosiforme Congénita
|
|
Descriptor Portuguese:
|
|
Eritrodermia Ictiosiforme Congênita
|
|
Synonyms English:
|
|
Congenital Ichthyosiform Erythroderma
|
|
Tree Number:
|
|
C16.131.831.512.400
C16.320.850.400
C16.614.492.400
C17.800.428.333.250
C17.800.804.512.400
C17.800.827.400
|
|
Definition English:
|
|
Designation for several severe forms of ichthyosis, present at birth, that are characterized by hyperkeratotic scaling. Infants may be born encased in a collodion membrane which begins shedding within 24 hours. This is followed in about two weeks by persistent generalized scaling. The forms include bullous (HYPERKERATOSIS, EPIDERMOLYTIC), non-bullous (ICHTHYOSIS, LAMELLAR), wet type, and dry type. |
|
Indexing Annotation English:
|
|
an ichthyosis rather than an erythroderma; do not use /congen & do not coord with INFANT, NEWBORN, DISEASES
|
|
History Note English:
|
|
91
|
|
Allowable Qualifiers English:
|
|
|
|
Record Number:
|
|
28985
|
|
Unique Identifier:
|
|
D016113
|
Occurrence in VHL:
|
|
|
Similar:
|
|
DeCS CID-10 SciELO LILACS LIS
|